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Relationship: 3134

Title

A descriptive phrase which clearly defines the two KEs being considered and the sequential relationship between them (i.e., which is upstream, and which is downstream). More help

Increase, Mitochondrial dysfunction leads to Increase, Cytotoxicity (renal tubular cell)

Upstream event
The causing Key Event (KE) in a Key Event Relationship (KER). More help
Downstream event
The responding Key Event (KE) in a Key Event Relationship (KER). More help

Key Event Relationship Overview

The utility of AOPs for regulatory application is defined, to a large extent, by the confidence and precision with which they facilitate extrapolation of data measured at low levels of biological organisation to predicted outcomes at higher levels of organisation and the extent to which they can link biological effect measurements to their specific causes.Within the AOP framework, the predictive relationships that facilitate extrapolation are represented by the KERs. Consequently, the overall WoE for an AOP is a reflection in part, of the level of confidence in the underlying series of KERs it encompasses. Therefore, describing the KERs in an AOP involves assembling and organising the types of information and evidence that defines the scientific basis for inferring the probable change in, or state of, a downstream KE from the known or measured state of an upstream KE. More help

AOPs Referencing Relationship

AOP Name Adjacency Weight of Evidence Quantitative Understanding Point of Contact Author Status OECD Status
Inhibition of mitochondrial DNA polymerase gamma leading to kidney toxicity adjacent High Low Angela Mally (send email) Under development: Not open for comment. Do not cite Under Development
Inhibition of mitochondrial electron transport chain (ETC) complexes leading to kidney toxicity adjacent Not Specified Not Specified Baki Sadi (send email) Under development: Not open for comment. Do not cite Under Development

Taxonomic Applicability

Latin or common names of a species or broader taxonomic grouping (e.g., class, order, family) that help to define the biological applicability domain of the KER.In general, this will be dictated by the more restrictive of the two KEs being linked together by the KER.  More help

Sex Applicability

An indication of the the relevant sex for this KER. More help

Life Stage Applicability

An indication of the the relevant life stage(s) for this KER.  More help

Key Event Relationship Description

Provides a concise overview of the information given below as well as addressing details that aren’t inherent in the description of the KEs themselves. More help

Mitochondria are an essential organelle in ROS production, ATP production, and have a crucial role in regulating both apoptotic and necrotic death (Bhatia, Capili, and Choi, 2020; Wang et al., 2016; Gao et al., 2019). This is particularly notable for renal tubular cells due to their high energy demands for filtration (Cohen, 1986). When mitochondria are damaged and their membrane potential is dissipated, the mitochondrial permeability transition pore (mPTP) is opened and they release cytochrome c (Cyt c), pro-apoptotic caspases, and apoptosis-inducing factor (AIF) (Mao et al., 2010; Galluzzi et al., 2018; Garrido et al., 2006). Cyt c is a protein that triggers apoptosis or necrosis by allosterically activating apoptosis-protease activating factor 1 (APAF 1) (Mao et al., 2010; Galluzzi et al., 2018; Garrido et al., 2006). APAF 1 is then able to cleave caspases 9 and 3, which lead to the induction of a caspase cascade that triggers apoptosis (Mao et al., 2010; Galluzzi et al., 2018; Garrido et al., 2006). Caspase-independent apoptosis is also triggered by the opening of the mPTP, causing the release of AIF which triggers DNA condensation into chromosomes and  degradation in a characteristic manner (Sevrioukova, 2011). Mitochondrial dysfunction therefore leads to not only further oxidative stress, but also to cell death (Bhatia, Capili, and Choi, 2020; Wang et al., 2016; Zhan et al., 2013).

Evidence Collection Strategy

Include a description of the approach for identification and assembly of the evidence base for the KER. For evidence identification, include, for example, a description of the sources and dates of information consulted including expert knowledge, databases searched and associated search terms/strings.  Include also a description of study screening criteria and methodology, study quality assessment considerations, the data extraction strategy and links to any repositories/databases of relevant references.Tabular summaries and links to relevant supporting documentation are encouraged, wherever possible. More help

Evidence Supporting this KER

Addresses the scientific evidence supporting KERs in an AOP setting the stage for overall assessment of the AOP. More help
Biological Plausibility
Addresses the biological rationale for a connection between KEupstream and KEdownstream.  This field can also incorporate additional mechanistic details that help inform the relationship between KEs, this is useful when it is not practical/pragmatic to represent these details as separate KEs due to the difficulty or relative infrequency with which it is likely to be measured.   More help

The evidence of biological plausibility between increased mitochondrial dysfunction and renal tubular cytotoxicity is strong, as it is detailed in numerous review articles (Bhatia, Capili, and Choi, 2020; Zhan et al., 2013; Gao et al., 2019; Garrido et al., 2006). Mitochondrial dysfunction includes the inhibition of calcium accumulation in the mitochondria, loss of mitochondrial membrane potential, the opening of the mitochondrial permeability transition pore, increased mitochondrial swelling, decreased ATP production, and mitochondrial depolarization (Bhatia, Capili, and Choi, 2020; Zhan et al., 2013; Gao et al., 2019; Garrido et al., 2006).

The induction of the permeability transition of the mitochondrial inner membrane in particular leads to the opening of the mitochondrial permeability transition pore (Mao et al., 2010). This allows the release of several pro-apoptotic molecules to the cytosol, including Cyt c, apoptosis-inducing factor (AIF), and the pro-caspases-2, -3, and -9 (Garrido et al., 2006). Mitochondrial dysfunction can trigger apoptosis through the use of caspase-dependant and independent pathways (Bhatia, Capili, and Choi, 2020; Zhan et al., 2013; Gao et al., 2019; Garrido et al., 2006).  The caspase-dependant pathway of apoptosis induction requires Cyt c. Cyt c is an electron carrier in the mitochondrial electron transport chain (Mao et al., 2010). When released from the mitochondrial it is able to allosterically activate a protein called apoptosis protease activating factor-1 (APAF-1) (Mao et al., 2010). APAF-1 is required for the proteolysis of caspases-9 and -3, which are able of inducing a caspase cascade that results in apoptosis (Mao et al., 2010). The opening of the MPTP is also able to induce a cascade-independent method of cell death via the protein AIF (Mao et al., 2010; Sevrioukova, 2011). AIF is a protein that is normally located on the inner mitochondrial membrane of the mitochondria (Sevrioukova, 2011). When released to the cytosol, AIF undergoes proteolysis and is transported to the nucleus of the cell and induces the condensation of chromatin, as well as characteristic degradation of the cell’s DNA to induce apoptosis in a caspase-independent manner (Sevrioukova, 2011)

Uncertainties and Inconsistencies
Addresses inconsistencies or uncertainties in the relationship including the identification of experimental details that may explain apparent deviations from the expected patterns of concordance. More help
  1. In an article studying the nephrotoxic effects of cisplatin treatment in rat kidneys, they found that treatment with 10 mg/kg bodyweight of cisplatin for 72 hours caused only a 0.3-fold decrease in the level of ATP content in the cell but induced a 1.8-fold increase in the level of executioner caspase-3 activity (Santos et al., 2007).
  2. In an article assessing the effects of depleted uranium on human kidney cells, mitochondrial membrane potential was increased significantly by only 3.9-fold when cells were treated with 500 μM for 24 hours (Hao et al., 2014). However, under the same conditions, cytotoxicity was elevated 6.5-fold. (Hao et al., 2014).
  3. A study assessing depleted uranium treatment on human embryonic kidney cells also found that only a 3.6-fold increase in membrane potential occurred for cells treated with depleted uranium, while a 5.6-fold increase was seen in cell death compared to the control (Hao et al., 2016).
  4. Another article investigated the effects of treatment with various heavy metal nanoparticles and micrometer particles on an alveolar type-II epithelial cell line. In addition, copper oxide nanoparticles and micrometer particles both showed 27.1-fold and 12.1-fold increases in mitochondrial depolarization while cytotoxicity was increased by 56.4-fold and 18.2-fold, respectively (Karlsson et al., 2009).

Known modulating factors

This table captures specific information on the MF, its properties, how it affects the KER and respective references.1.) What is the modulating factor? Name the factor for which solid evidence exists that it influences this KER. Examples: age, sex, genotype, diet 2.) Details of this modulating factor. Specify which features of this MF are relevant for this KER. Examples: a specific age range or a specific biological age (defined by...); a specific gene mutation or variant, a specific nutrient (deficit or surplus); a sex-specific homone; a certain threshold value (e.g. serum levels of a chemical above...) 3.) Description of how this modulating factor affects this KER. Describe the provable modification of the KER (also quantitatively, if known). Examples: increase or decrease of the magnitude of effect (by a factor of...); change of the time-course of the effect (onset delay by...); alteration of the probability of the effect; increase or decrease of the sensitivity of the downstream effect (by a factor of...) 4.) Provision of supporting scientific evidence for an effect of this MF on this KER. Give a list of references.  More help

There are several known modulating factors that affect the relationship between mitochondrial dysfunction and cell death. One known modulating factor of this variation is mitochondrial biogenesis (Jornayvaz and Shulman, 2010). Mitochondrial biogenesis is the ratio of growth, division, and recycling of existing mitochondria in the cell. Mitochondrial biogenesis itself is influenced by a variety of factors such as exercise levels, cell division, low temperature, caloric restriction, and as is discussed in this AOP, oxidative stress . As a result of changes in these factors, the mitochondrial content, as well as sizes and masses of each of the organelles, is altered . For example, it is generally accepted that increased exercise in an organism increases mitochondrial content and functioning, as there is an increased energy need in those organisms . Therefore, an organism with increased exercise habits would have a less steep slope in the relationship between mitochondrial dysfunction and cell death, as the mitochondrial dysfunction would not be able cause cell death as quickly, since mitochondrial content would be higher requiring a longer time period to accumulate sufficiently to induce apoptosis . This would allow the cell to undergo mitophagy of the injured mitochondria while still continuing to produce adequate energy to keep the cell alive . Similarly, if a cell had just divided, it would be less prepared and capable of dealing with mitochondrial dysfunction, which would allow it to accumulate much faster and would therefore increase the slope between mitochondrial dysfunction and cell death (Jornayvaz and Shulman, 2010).

Some diseases are also known to modulate this relationship, such as early aging and diabetes (Pizzorno, 2014). These diseases increase the slope of the relationship between mitochondrial dysfunction leading to oxidative stress due to the fact that they induce faster accumulation of mitochondrial dysfunction via increased levels of oxidative stress and faster accumulation of mitochondrial DNA damage leading to earlier mitochondrial dysfunction (Nissanka and Moraes, 2018; Zelenka, Dvorak, and Alan, 2015; Wei et al., 2015; Kudryavtseva et al., 2016; Forbes and Thorburn, 2018; Schiffer and Friederich-Persson, 2017).

Response-response Relationship
Provides sources of data that define the response-response relationships between the KEs.  More help

There is a strong, positive correlation between the increase in mitochondrial dysfunction and the increase in cytotoxicity. This was demonstrated by an article which plotted MTT cell viability assay results and LDH concentration in the cell culture media which showed a negative correlation with a slope of -0.99 and a correlation coefficient of 0.97 (Wang et al., 2016).

Time-scale
Information regarding the approximate time-scale of the changes in KEdownstream relative to changes in KEupstream (i.e., do effects on KEdownstream lag those on KEupstream by seconds, minutes, hours, or days?). More help

There has not yet been an identified time-scale for this relationship. Further research will be required in order to determine the time-scale.

Known Feedforward/Feedback loops influencing this KER
Define whether there are known positive or negative feedback mechanisms involved and what is understood about their time-course and homeostatic limits. More help

There are no feedforward or feedback loops that are known to influence this KER.

Domain of Applicability

A free-text section of the KER description that the developers can use to explain their rationale for the taxonomic, life stage, or sex applicability structured terms. More help

The domain of applicability only includes vertebrates, as invertebrates and non-animals do not have kidneys (Mahasen, 2016).

References

List of the literature that was cited for this KER description. More help

Belyaeva, E. A., Sokolova, T. V., Emelyanova, L. V., & Zakharova, I. O. (2012). Mitochondrial

electron transport chain in heavy metal-induced neurotoxicity : Effects of cadmium , mercury , and copper. Thescientificworld, 2012, 1-14. doi:10.1100/2012/136063

Bhatia, D., Capili, A., & Choi, M. E. (2020). Mitochondrial dysfunction in kidney injury,

inflammation, and disease; potential therapeutic approaches. Kidney Res. Clin. Pract., 39(3), 244-258. doi:10.23876/j.krcp.20.082

Cohen, J. J. (1986). Relationship between energy requirements for na reabsorption and other

renal functions. Kidney International, 29(1), 32-40. doi:10.1038/ki.1986.5

Forbes, J. M., & Thorburn, D. R. (2018). Mitochondrial dysfunction in diabetic kidney

disease. Nature Review Nephrology, 14(5), 291. doi:10.1038/nrneph.2018.9

Gao, N., Huang, Z., Liu, H., Hou, J., & Liu, X. (2019). Advances on the toxicity of uranium to

different organisms. Chemosphere, 237, 124548. doi:10.1016/j.chemosphere.2019.124548

Galluzzi, L., Vitale, I., Aaronson, S., & et al. (2018). Molecular mechanisms of cell death:

Recommendations of the nomenclature committee on cell death 2018. Cell Death and Differentiation, 25, 486-541. doi:10.1038/s41418-017-0012-4

Garrido, C., Galluzzi, L., Brunet, M., Puig, P. E., Didelot, C., & Kroemer, G. (2006).

Mecxhanisms of cytochrome c release from mitochondria. Cell Death and Differentiation, 13, 1423-1433. doi:10.1038/sj.cdd.4401950

Hao, Y., Huang, J., Liu, C., Li, H., Liu, J., Zeng, Y., . . . Li, R. (2016). Differential protein

expression in metallothionein protection from depleted uranium-induced nephrotoxicity. Scientific Reports, doi:10.1038/srep38942

Hao, Y., Ren, J., Liu, C., Li, H., Liu, J., Yang, Z., . . . Su, Y. (2014). Zinc protects human kidney

cells from depleted uranium induced apoptosis. Basic & Clinical Pharmacology & Toxicology, 114, 271-280. doi:10.1111/bcpt.12167

Hassani, S., Yaghoubi, H., Khosrokhavar, R., Jafarian, I., Mahayekhi, V., Housseini, M., &

Shahraki, J. (2015). Mechanistic view for toxic effects of arsenic on isolated rat kidney and brain mitochondria. Biologia, 70(5), 683-689. doi:10.1515/biolog-2015-0081

Jornayvaz, F. R., & Shulman, G. I. (2010). Regulation of mitochondrial biogenesis. Essays

Biochem., 47, 69-84. doi:10.1042/bse0470069

Karlsson, H. L., Gustafsson, J., Cronholm, P., & Möller, L. (2009). Size-dependent toxicity of

metal oxide particles—A comparison between nano- and micrometer size. Toxicology Letters, 188(2), 112-118. doi:10.1016/j.toxlet.2009.03.014

Kruidering, M., Van De Water, B., De Heer, E., Mulder, G. J., & Nagelkerke, J. F. (1997).

Cisplatin-induced nephrotoxicity in porcine proximal tubular cells: Mitochondrial dysfunction by inhibition of complexes I to IV of the respiratory chain. The Journal of Pharmacology and Experimental Therapeutics, 280(2), 638-649.

Kudryavtseva, A. V., Krasnov, G. S., Dmitriev, A. A., Alekseev, B. Y., Kardymon, O. L.,

Sadritdinova, A. F., . . . Snezhkina, A. V. (2016). Mitochondrial dysfunction and oxidative stress in aging and cancer. Oncotarget, 7(29), 44879-44905. doi:10.18632/oncotarget.9821

Mahasen, L. M. A. (2016). Evolution of the kidney. Anatomy Physiol. Biochem. Int. J., 1(1),

555554. doi:10.19080/APBIJ.2016.01.555554

Mao, W., Zhang, N. N., Zhou, F. Y., Li, W. X., Liu, H. Y., Feng, J., . . . He, Z. J. (2010).

Cadmium directly induced mitochondrial dysfunction of human embryonic kidney cells. Human and Experimental Toxicology, 30(8), 920-929. doi:10.1177/0960327110384286

Miyayama, T., Arai, Y., Suzuki, N., & Hirano, S. (2013). Mitochondrial electron transport is

inhibited by disappearance of metallothionein in human bronchial epithelial cells follwoing exposure to silver nitrate. Toxicology, 305, 20-29. doi:10.1016/j.tox.2013.01.004

Nissanka, N., & Moraes, C. T. (2018). Mitochondrial DNA damage and reactive oxygen species

in neurodegenerative disease. FEBS Lett., 592(5), 728-742. doi:10.1002/1873-3468.12956

Pizzorno, J. (2014). Mitochondria - fundamental to life and health. Integrative Medicine

(Encinitas), 13(2), 8-15.

Santos, N. A. G., Catão, C. S., Martins, N. M., Curti, C., Bianchi, M. L. P., & Santos, A. C.

(2007). Cisplatin-induced nephrotoxicity is associated with oxidative stress, redox state unbalance, impairment of energetic metabolism and apoptosis in rat kidney mitochondria. Archives of Toxicology, 81(7), 495-504. doi:10.1007/s00204-006-0173-2

Schiffer, T. A., & Friederich-Persson, M. (2017). Mitochondrial reactive oxygen species and

kidney hypoxia in the development of diabetic nephropathy. Front. Physiol., 8:211. doi:10.3389/fphys.2017.00211

Sevrioukova, I. F. (2011). Apoptosis-inducing factor: Structure, function, and redox

regulation. Antioxid Redox Signal., 14(12), 2545-2579. doi:10.1089/ars.2010.3445

Shaki, F., Hosseini, M. J., Ghazi-Khansari, M., & Pourahmad, J. (2012). Toxicity of depleted

uranium on isolated rat kidney mitochondria. Biochimica Et Biophysica Acta - General Subjects, 1820(12), 1940-1950. doi:10.1016/j.bbagen.2012.08.015

Thiébault, C., Carrière, M., Milgram, S., Simon, A., Avoscan, L., & Gouget, B. (2007). Uranium

induces apoptosis and is genotoxic to normal rat kidney (NRK-52E) proximal cells. Toxicological Sciences : An Official Journal of the Society of Toxicology, 98(2), 479-487. doi:kfm130 [pii]

Wang, Y., Wang, S., Jia, L., Zhang, L., Ba, J., Han, D., . . . Wu, Y. (2016). Nickel-refining

fumes induced DNA damage and apoptosis of NIH/3T3 cells via oxidative stress. International Journal of Environmental Research and Public Health, 13(7), 629-644. doi:10.3390/ijerph13070629

Wei, Y., Zhang, Y., Cai, Y., & Xu, M. (2015). The role of mitochondria in mTOR-regulated

longevity. Biol. Rev., 90, 167-181. doi:10.1111/brv.12103

Zelenka, J., Dvorak, A., & Alan, L. (2015). L-lactate protects skin fibroblasts against aging-

asociated mitochondrial dysfunction via mitohormesis. Oxidative Medicine and Cellular Longevity, 2015 doi:10.1155/2015/351698

Zhan, M., Brooks, C., Liu, F., Sun, L., & Zheng, D. (2013). Mitochondrial dynamics: Regulatory

mechanisms and emerging role in renal pathophysiology. Kidney International, 83, 568-581. doi:10.1038/ki.2012.441

Zhang, H., Chang, Z., Mehmood, K., Abbas, R. Z., Nabi, F., Rehman, M. U., . . . Zhou, D.

(2018). Nano copper induces apoptosis in PK-15 cells via a mitochondria-mediated pathway. Biological Trace Element Research, 181(1), 62-70. doi:10.1007/s12011-017-1024-0